Proceso de atención de enfermería en fibrosis quística según el Modelo de Callista Roy

Abstract

Cystic fibrosis (CF) is caused by mutations in the CF transmembrane conductance regulator located on chromosome 7, which functions to conduct chloride ions across the epithelial cell membrane. Genetic changes cause alterations in this transport, producing thick secretions in the lungs, alterations in the liver, intestines, pancreas and even in the reproductive system; it is considered a potentially fatal recessive genetic pathology, which is more common among white people, limiting their lives. The incidence is 1 in 1800-2500 live births, and heterozygous carriers represent 1 in 40 to 50 in Caucasians.in Ecuador its incidence is 1 in 11500 births, identifying 200 cases value that could increase, being CF a little known disease and often misdiagnosed. It manifests with persistent cough, wheezing and through X-ray examination reveals pulmonary hyperinflation and obstruction of the lower airways and in its severe stage presents with exacerbations, pulmonary in recurrent acute clinical pictures